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1.SPRENGEL SHOULDER.pptx

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1.SPRENGEL SHOULDER.pptx

  1. 1. SPRENGEL SHOULDER
  2. 2. • IN THIS CONDITION SCAPULA FAILS TO DESCEND DOWN FROM ITS INITIAL HIGH POSITION IN THE EMBRYO • HERE THE SCAPULA LIES MORE SUPERIORLY. IT IS HYPOPLASTIC AND IMPROPERLY SHAPED • IT IS ASSOCIATED WITH OTHER CONGENITAL ANOMALIES LIKE CERVICAL RIB, ETC.
  3. 3. ETIOLOGY: • THIS MAY BE DUE TO IMPERFECT DESCENT OF THE SHOULDER GIRDLE BY THIRD MONTH OR A BAND OF MUSCLE FROM THE SKULL TO THE SCAPULA WHICH HAS FAILED TO GROW.
  4. 4. CLINICAL FEATURES: • THE SCAPULAR MUSCLES ARE POORLY DEVELOPED AND MAY BE REPRESENTED BY FIBROUS BANDS. • IT MAY BE ACCOMPANIED BY SCOLIOSIS (THORACIC CURVE) WITH CONVEXITY ON THE INVOLVED SIDE. • THE MOVEMENT OF SCAPULA IS MARKEDLY LIMITED DUE TO THE FIBROUS BANDS OR A BONY BAR RESULTING IN LIMITATION OF SHOULDER ABDUCTION AND ELEVATION. • HOWEVER, THE FUNCTIONAL DISABILITY IS USUALLY MINIMAL. • VERY LITTLE IMPROVEMENT CAN BE OFFERED BY WAY OF CORRECTIVE EXERCISES
  5. 5. • THE SCAPULA IS HIGH BY 2 TO 10 CM, THE DEFORMITY IS OBVIOUS • CAVENDISH’S GRADING • GROUP 1—VERY MILD • GROUP 2—MILD, SHOULDER SLIGHTLY UNALIGNED • GROUP 3—MODERATE, SHOULDER HIGH. • GROUP 4—SEVERE, WITH SUPERIOR ANGLE OF SCAPULA NEAR THE OCCIPUT.
  6. 6. INVESTIGATION: • PLAIN X-RAY
  7. 7. TREATMENT: • FOR CASES WITH MILD DEFORMITY NO TREATMENT IS REQUIRED. • FOR SEVERE CASES SURGERY IS DONE AFTER 3 YEARS AND THIS CONSISTS OF RELEASE OF MUSCLES FROM THE SCAPULA OR TRANSFER OF ORIGIN OF THE TRAPEZIUS MUSCLE
  8. 8. PT MANAGEMENT: • MEASURES TO CONTROL PAIN • USUAL METHODS LIKE ULTRASONIC, TENS, ETC. ARE HELPFUL. • MEASURES FOR MOBILIZATION • GENTLE RELAXED PASSIVE MOVEMENTS OF THE SHOULDER GIRDLE MUSCLES. • EARLY MOBILITY OF THE SHOULDER IS AIMED AT. • MEASURES TO STRENGTHEN THE MUSCLES • THE MUSCLES AROUND THE SHOULDER GIRDLE ARE STRENGTHENED BY SUITABLE ISOMETRIC AND ISOTONIC SHOULDER EXERCISES

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