pediatric neurology mcq for ug

1. Pediatric neurology
Hari Shankar Meshram

2. Boring topic that too in afternoon

3. Waiting for the last slide

4. For passing marks
LP finding in APM and TBM
Apm : very low glucose, neutrophilic, very high
protein
Tbm : low glucose, lymphocytic, high protein,
cob web appearance

5. Neurofibromatosis has all of the following
except
1. Crowe sign
2. Lisch nodule
3. Brushfield iris
4. Neurofibroma
3

6. Recent
Tuberous sclerosis has all skin lesion except
1. Ash leaf macule
2. Adenoma sebacium
3. Shagreen patch
4. Angel kiss
4

7. Reversible gallbaldder sludge detected by
USG during treatment of bacterial
meningitis is caused by
1. Ceftriaxone
2. Cefotaxime
3. Vancomycin
4. Meropenem
1

8. Floppy baby
Spinal muscular dystrophy important genetic
cause of floppy baby invloves chromosome
1. 5
2. 6
3. 7
4. 9
1

9. AFP
Transverse myleitis involves mostly
1. Thoracic
2. Lumbar
3. Lumbosacral
4. Cervical
1 Afp causes are
polio, gullian barre
,transverse myelitis,
traumatic neuritis

10. floppy
Almond shaped eyes , with hyperphagia ,and
obesity and hypogonadism and history of
hypotonia in newborn period
1. Angelman
2. Prader willi
3. Gaucher
4. Tay Sach
2

11. Anterior fontonalle closes at months
1. 2 -3
2. 4-7
3. 9-12
4. 18-24
4

12. Total volume of CSF in neonate is
1. 50 ml
2. 100 ml
3. 25 ml
4. 150 ml
1 and 2 in
adult

13. Neural tube and neural migration
Which of the following is neuronal migration
defect
1. Shizencephaly
2. Myelomeningocele
3. SSPE
4. Gaucher
1

14. True about hydranencephaly
1.Absent cerebral hemisphere
2. Sun setting sign
3.Mental retardation
4.Normal sized ventricle
1

15. Hydranencephaly

16. CSF production rate per hour is
1. 20 ml
2. 10 ml
3. 25 ml
4. 15 ml
1

17. Normal ICP in a child is mmH20
1. 30 – 70
2. 50 – 80
3. 100 -150
4. 50 – 150
2 And 4 answer in case of adult

18. Choose one
1. 3.
2.
4. All of the above

19. Development
Razing at what age
1. 4 m
2. 6
3. 8
4. 10
1

20. Neck control at what age
1. 3
2. 6
3. 8
4. 10
1

21. Recently asked
9 cube tower at what age month
1. 40
2. 30
3. 20
4. 15
Answer is 2.
2 cubes 15 month
4 cubes 18 month
6 cubes 22 month
7 cubes 24
9 cube 30
10 cube 36 month

22. Casting at what age
1. 10 month
2. 6
3. 8
4. 12
4 casting means
throwing things

23. Mouthing and stranger anxiety and moros reflex
should disapper at what age
1. 4
2. 6
3. 8
4. 10
2

24. Object permenance, peek a boo game , waves bye
bye , and immature pincer grasp at what age
1. 4
2. 6
3. 9
4. 10
3

25. Separational anxiety, transitional object at what
age
1. 12
2. 18
3. 15
4. 10
2

26. 13yr old child presented with fever and
altered sensorium with MRI shwoing
medial temporal lobe involvement
1. HSV
2. Neisseria
3. Cerebral malaria
4. Fungal meningitis
1

27. • Most common neurological sequele in
bacterial meningitis
1.Recurrent seizures
2 Hearing loss
3 Cognitive loss
4 Visual loss
2

28. Excessive irritability, crying,vomiting and
difficulty feeding with history of frequent
change in formula feeds suggests
1. Tay sach disease
2. Krabbes disease
3. Metachromatic leucodystrophy
4.Gaucher disease
2

29. A child with painful acroparastheisa and
angiokeratoma in skin with zebra bodies and
maltese cross in urine sample suggests
1. Tay sach disease
2. Krabbes disease
3. Fabry disease
4.Gaucher disease
3

30. Recent
• Seizures with aphasia as abnormal finding is
seen in
1. Absence seizures
2. West syndrome /Infantile spasm
3. Rolandic seizures
4. Landau klefner syndrome
4

31. Recent
• Hypsarrythmia is seen in
1. Absence seizures
2. West syndrome /Infantile spasm
3. Rolandic seizures
4. Landau klefner syndrome
2

32. Recent
• Periodic lateralised slowing in EEG is seen in
1. Absence seizures
2. Herpes simplex meningitis
3. Rolandic seizures
4. Landau klefner syndrome
2

33. Recent
• Multiple seizures of all types is seen in
1. Lennox gestaut syndrome
2. West syndrome /Infantile spasm
3. Rolandic seizures
4. Landau klefner syndrome
1

34. Choose one
1. 3.
2. 4. All of the above

35. Recent
• Lafora disease has
1. Absence seizures
2. Infantile spasm
3. myoclonic seizures
4. GTCS
3

36. Kernicterus in neonatal period is a major cause
of
1. Spastic diplegia CP
2. Spastic hemiplegia CP
3. Spastic quadriplegia CP
4. Athetoid CP
4

37. Most important risk factors for reurrence of
febrile seizures is
1. Age < 2 yrs
2. Family History
3. Seizures at peak of fever
4. Long prolonged fever before seizure
2

38. Passing mark q Cerebral palsy
Cerebral palsy in which upper limb is more affected
than lower limb is
1. Spastic diplegia CP
2. Spastic paraplegia CP
3. Spastic quadriplegia CP
4. Athetoid CP
1

39. Prematurity is a major cause of
1. Spastic diplegia CP
2. Spastic hemiplegia CP
3. Spastic quadriplegia CP
4. Athetoid CP
1

40. Birth asphyxia is a major cause of
1. Spastic diplegia CP
2. Spastic hemiplegia CP
3. Spastic quadriplegia CP
4. Athetoid CP
3

41. A newborn presents with prominent
hiccups,seizures and lethargy progressing to
coma
1. Nonketotic hyperglycenemia
2. Alexander disease
3. Maple syrup disease
4. Canavan disease
1

42. A 10 yr child with macrocephaly and
developmental delay and frontal region
changes in MRI suggests
1. Nonketotic hyperglycenemia
2. Alexander disease
3. Maple syrup disease
4. Canavan disease
2

43. A 10 yr child with seizures and developmental
delay and parietocccipital changes in MRI
suggests
1. X linked adrenoleucodystrophy
2. Alexander disease
3. Maple syrup disease
4. Canavan disease
1

44. Very long chain fatty acid is elevated and is
diagnostic in
1. X linked adrenoleucodystrophy
2. Alexander disease
3. Maple syrup disease
4. Canavan disease
1

45. Lorenzo oil is used in treatment of
1. X linked adrenoleucodystrophy
2. Alexander disease
3. Refsum Disease
4. Canavan disease
3

46. 11yr child with suspected inborn error of
metabolism and hyperammonimia
1. X linked adrenoleucodystrophy
2. Maple syrup disease
3. Organic aciduria
4. Urea cycle defect
4

47. Drugs for treatment of partial seizures
1. Valproate
2. Carbamazepine
3. Phenytoin
4. Phenobarbitone
1

48. Recent
SSPE is diagnosed by all except
1. EEG
2. Brain biopsy
3. Antibody of measles in blood
4. Antibodies in CSF.
3

49. Cerebral palsy with most seizures is
1. Spastic diplegia CP
2. Spastic hemiplegia CP
3. Spastic quadriplegia CP
4. Athetoid CP
1

50. Swallowing develops at weeks of gestation
1. 10
2. 12
3. 14
4. 16
2

51. Recent asked
Eye lid opening at what gestational age
1. 24 week
2. 26
3. 28
4. 20
2

52. Prader willi syndrome is suspected in a floppy
infant and involved chromosome is
1. 10
2. 12
3. 15
4. 16
3

53. Angelman syndrome is suspected in a female
with over friendly and happy puppet face is
having chromosome involved
1. 10
2. 12
3. 15
4. 16
3

54. Thanks
N
Happy vacation