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Nystagmus
                                                       Causes in infants and children

o   Slow < 40 jerks / min                                 o   Albinism
o   Fast > 100 jer / min                                  o   Bilateral optic nerve hypoplasia = morsier’s
                                                              syndrome
                                                          o   Bilateral media opacities
                                                          o   Achromatopsia
So κ.φ= 40 – 100 jerks /min
                                                          o   Retinitis pigmentosA = USHER’S SYNDROME



Amplitude
    o   Fine < 1mm
    o   Coarse > 3mm



Involvement
    o   Bilateral eyes
    o   Unilateral eye




ABSENT NYSTAGMUS IN ACUTE SEVERE
VERTIGO IS UNUSUAL


Normal findings
    o   Lateral gaze nystagmus



Ubnormal findings
    o   Spontaneous or front gaze nystagmus
    o   Horizontal = peripheral disease = unilateral
        vestibular pathology



    o   Vertical = CNS = brain stem lesion

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27 Nystagmus

  • 1. Nystagmus Causes in infants and children o Slow < 40 jerks / min o Albinism o Fast > 100 jer / min o Bilateral optic nerve hypoplasia = morsier’s syndrome o Bilateral media opacities o Achromatopsia So κ.φ= 40 – 100 jerks /min o Retinitis pigmentosA = USHER’S SYNDROME Amplitude o Fine < 1mm o Coarse > 3mm Involvement o Bilateral eyes o Unilateral eye ABSENT NYSTAGMUS IN ACUTE SEVERE VERTIGO IS UNUSUAL Normal findings o Lateral gaze nystagmus Ubnormal findings o Spontaneous or front gaze nystagmus o Horizontal = peripheral disease = unilateral vestibular pathology o Vertical = CNS = brain stem lesion