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Non cyanotic Congenital heart diseases

                         C Bussadori (Milano,IT)

 Department of Pediatric Cardiology and Adult with Congenital Heart Disease
   p                             gy                   g
                       IRCCS- Policlinico San Donato
                    San Donato Milanese – Milano Italy




                           EUROECHO CONGRESS - COPENHAGEN -
                                 TEACHING COURSE 2010
ASD Ostium secundum
The Most Common atrial septal defect

 – Various size
 – Parasternal Short axis
 – Subcostal view
    • Suboptimal in adults




                       EUROECHO CONGRESS - COPENHAGEN -
                             TEACHING COURSE 2010
ASD Ostium secundum
The Most Common atrial septal defect

    – Modified apical 4 ch
    – Various size
    – CFD
        • Beware to high RA pressure




                          EUROECHO CONGRESS - COPENHAGEN -
                                TEACHING COURSE 2010
ASD Ostium secundum
   The Most Common atrial septal defect
It seem circular but often it isn’t
   – Measure from different views and consider
     the largest
   – 3D it helps
   – TEE 2D or 3D offer ultimate sizing for ASD
     and rim diameters




                            EUROECHO CONGRESS - COPENHAGEN -
                                  TEACHING COURSE 2010
ASD Ostium secundum
 The Most Common atrial septal defect

It seem circular but often it isn’t
   – TEE 2D or 3D offer ultimate
     information on ASD and rims
     shape and dimension




                           EUROECHO CONGRESS - COPENHAGEN -
                                 TEACHING COURSE 2010
ASD Differential Diagnosis: OS 1
Partial AV septal defect
AV valve at the same level: MR, goose neck deformity of LVOT
Post Surgical Complication: SAS Complete AV block
     S gical Complication SAS,




                         EUROECHO CONGRESS - COPENHAGEN -
                               TEACHING COURSE 2010
ASD Differential Diagnosis:
Sinus Venous Defects
•   Difficult to diagnose by TTE
•   Modified parasternal
•   Subcostal
•   Often associate to
    Anomalous pulmonary
    venous drainage




                            EUROECHO CONGRESS - COPENHAGEN -
                                  TEACHING COURSE 2010
Ventricular septal defect
• Perimembranous
  – Various estension


• Muscular
  –I l
    Inlet, O l
           Outlet, apical
                     i l
    trabecular
  – Doubly committed
    Subarterial


                    EUROECHO CONGRESS - COPENHAGEN -
                          TEACHING COURSE 2010
Perimembranous VSD




             EUROECHO CONGRESS - COPENHAGEN -
                   TEACHING COURSE 2010
Perimembranous VSD
TTE                    TEE




           EUROECHO CONGRESS - COPENHAGEN -
                 TEACHING COURSE 2010
Perimembranous VSD
2D TEE                       3D TEE




              EUROECHO CONGRESS - COPENHAGEN -
                    TEACHING COURSE 2010
Perimembranous VSD




     EUROECHO CONGRESS - COPENHAGEN -
           TEACHING COURSE 2010
Perimembranous VSD




     EUROECHO CONGRESS - COPENHAGEN -
           TEACHING COURSE 2010
Perimembranous VSD




           EUROECHO CONGRESS - COPENHAGEN -
                 TEACHING COURSE 2010
Muscular VSD
•Apical Trabecular
 Apical
    •4 chamber
•Muscular Inlet
    •Short Axis
•Multiple VSD
 M lti l
    •3D




                     EUROECHO CONGRESS - COPENHAGEN -
                           TEACHING COURSE 2010
Doubly committed Subarterial
Fibrous continuty
  between aortic and
  pulmonary valves




              EUROECHO CONGRESS - COPENHAGEN -
                    TEACHING COURSE 2010
PDA
              • Most of adult cases of
                PDA are small and
                silent
              • Parasternal short axis
                view
              • CFM Demonstrate L to
                R Shunt from PDA to
                   Sh t f          t
                MPA
              • CW Doppler reflects
                PA pressure




EUROECHO CONGRESS - COPENHAGEN -
      TEACHING COURSE 2010
Aortic coarctation
•   Between left subclavian and arterial
    duct
•   Frequently assoc ated to
      eque t y associated
•   PDA, VSD, Ao.Bic.
•   Modified Bernoulli formula
•   (ΔP=4(v
    (ΔP 4( 22 – v12))
•   CW peack gradient. Mean Gradient 
•   PW abdominal aorta




                                                           V1


                                                           V2




                             EUROECHO CONGRESS - COPENHAGEN -
                                   TEACHING COURSE 2010
Aortic bicuspidia
            p




             EUROECHO CONGRESS - COPENHAGEN -
                   TEACHING COURSE 2010
Aortic bicuspidia




             EUROECHO CONGRESS - COPENHAGEN -
                   TEACHING COURSE 2010
Aortic regurgitation




            EUROECHO CONGRESS - COPENHAGEN -
                  TEACHING COURSE 2010
Sinus of Valsalva Perforation
Pulmonic Stenosis
Various Morphology




           *Milo S Heart 1988;60:128-133



  80% are dome shaped
                  p
Pulmonic stenosis




            EUROECHO CONGRESS - COPENHAGEN -
                  TEACHING COURSE 2010
Pulmonic stenosis




            EUROECHO CONGRESS - COPENHAGEN -
                  TEACHING COURSE 2010
PS “hour-glass”
Take home a message
                      g
• Non cyanotic CHD could be an unexpected
       y                           p
 diagnosis in an adult cardiac patient

• Recognize the anatomical features and
 pathophysiological changes t suggest
   th h i l i l h           to      t
 appropriate treatment and Follow UP




               EUROECHO CONGRESS - COPENHAGEN -
                     TEACHING COURSE 2010

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Euroecho2010 non-cyanotic-disease

  • 1. Non cyanotic Congenital heart diseases C Bussadori (Milano,IT) Department of Pediatric Cardiology and Adult with Congenital Heart Disease p gy g IRCCS- Policlinico San Donato San Donato Milanese – Milano Italy EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 2. ASD Ostium secundum The Most Common atrial septal defect – Various size – Parasternal Short axis – Subcostal view • Suboptimal in adults EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 3. ASD Ostium secundum The Most Common atrial septal defect – Modified apical 4 ch – Various size – CFD • Beware to high RA pressure EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 4. ASD Ostium secundum The Most Common atrial septal defect It seem circular but often it isn’t – Measure from different views and consider the largest – 3D it helps – TEE 2D or 3D offer ultimate sizing for ASD and rim diameters EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 5. ASD Ostium secundum The Most Common atrial septal defect It seem circular but often it isn’t – TEE 2D or 3D offer ultimate information on ASD and rims shape and dimension EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 6. ASD Differential Diagnosis: OS 1 Partial AV septal defect AV valve at the same level: MR, goose neck deformity of LVOT Post Surgical Complication: SAS Complete AV block S gical Complication SAS, EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 7. ASD Differential Diagnosis: Sinus Venous Defects • Difficult to diagnose by TTE • Modified parasternal • Subcostal • Often associate to Anomalous pulmonary venous drainage EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 8. Ventricular septal defect • Perimembranous – Various estension • Muscular –I l Inlet, O l Outlet, apical i l trabecular – Doubly committed Subarterial EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 9. Perimembranous VSD EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 10. Perimembranous VSD TTE TEE EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 11. Perimembranous VSD 2D TEE 3D TEE EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 12. Perimembranous VSD EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 13. Perimembranous VSD EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 14. Perimembranous VSD EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 15. Muscular VSD •Apical Trabecular Apical •4 chamber •Muscular Inlet •Short Axis •Multiple VSD M lti l •3D EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 16. Doubly committed Subarterial Fibrous continuty between aortic and pulmonary valves EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 17. PDA • Most of adult cases of PDA are small and silent • Parasternal short axis view • CFM Demonstrate L to R Shunt from PDA to Sh t f t MPA • CW Doppler reflects PA pressure EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 18. Aortic coarctation • Between left subclavian and arterial duct • Frequently assoc ated to eque t y associated • PDA, VSD, Ao.Bic. • Modified Bernoulli formula • (ΔP=4(v (ΔP 4( 22 – v12)) • CW peack gradient. Mean Gradient  • PW abdominal aorta V1 V2 EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 19. Aortic bicuspidia p EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 20. Aortic bicuspidia EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 21. Aortic regurgitation EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 22. Sinus of Valsalva Perforation
  • 23. Pulmonic Stenosis Various Morphology *Milo S Heart 1988;60:128-133 80% are dome shaped p
  • 24. Pulmonic stenosis EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 25. Pulmonic stenosis EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010
  • 27. Take home a message g • Non cyanotic CHD could be an unexpected y p diagnosis in an adult cardiac patient • Recognize the anatomical features and pathophysiological changes t suggest th h i l i l h to t appropriate treatment and Follow UP EUROECHO CONGRESS - COPENHAGEN - TEACHING COURSE 2010